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Gene | KIT |
Variant | M541L |
Impact List | missense |
Protein Effect | unknown |
Gene Variant Descriptions | KIT M541L lies within the transmembrane domain of the Kit protein (PMID: 16226710). M541L is a common polymorphism that has been demonstrated to increase proliferation in the presence of ligand compared to wild-type Kit in culture (PMID: 18795925), but is not associated with tumorigenesis in the population (PMID: 16307017, PMID: 21757432), and therefore, its effect on Kit protein function is unknown. |
Associated Drug Resistance | |
Category Variants Paths |
KIT mutant KIT M541L |
Transcript | NM_000222.3 |
gDNA | chr4:g.54727298A>C |
cDNA | c.1621A>C |
Protein | p.M541L |
Source Database | RefSeq |
Genome Build | GRCh38/hg38 |
Transcript | gDNA | cDNA | Protein | Source Database | Genome Build |
---|---|---|---|---|---|
NM_000222 | chr4:g.54727298A>C | c.1621A>C | p.M541L | RefSeq | GRCh38/hg38 |
NM_000222.3 | chr4:g.54727298A>C | c.1621A>C | p.M541L | RefSeq | GRCh38/hg38 |
NM_001385285.1 | chr4:g.54727298A>C | c.1621A>C | p.M541L | RefSeq | GRCh38/hg38 |
NM_000222.2 | chr4:g.54727298A>C | c.1621A>C | p.M541L | RefSeq | GRCh38/hg38 |
XM_017008178 | chr4:g.54727298A>C | c.1621A>C | p.M541L | RefSeq | GRCh38/hg38 |
XM_017008178.1 | chr4:g.54727298A>C | c.1621A>C | p.M541L | RefSeq | GRCh38/hg38 |
Molecular Profile | Indication/Tumor Type | Response Type | Therapy Name | Approval Status | Evidence Type | Efficacy Evidence | References |
---|---|---|---|---|---|---|---|
KIT M541L | chronic leukemia | sensitive | Imatinib | Phase I | Actionable | In Phase I trials, KIT M541L has been associated with response to Gleevec (imatinib) in chronic eosinophilic leukemia, NOS (PMID: 25015329) and mastocytosis (PMID: 18795925). | 25015329 18795925 |