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Gene | IDH1 |
Variant | R132C |
Impact List | missense |
Protein Effect | gain of function |
Gene Variant Descriptions | IDH1 R132C lies within the active site of the Idh1 protein (PMID: 19228619). R132C confers a gain of function to Idh1 as indicated by conversion of alpha-ketoglutarate to the onco-metabolite 2HG (R(-)-2-hydroxyglutarate in culture (PMID: 19935646, PMID: 26161668, PMID: 22885298). |
Associated Drug Resistance | |
Category Variants Paths |
IDH1 mutant IDH1 act mut IDH1 R132C IDH1 mutant IDH1 R132X IDH1 R132C |
Transcript | NM_005896.4 |
gDNA | chr2:g.208248389G>A |
cDNA | c.394C>T |
Protein | p.R132C |
Source Database | RefSeq |
Genome Build | GRCh38/hg38 |
Transcript | gDNA | cDNA | Protein | Source Database | Genome Build |
---|---|---|---|---|---|
NM_001282386.1 | chr2:g.208248389G>A | c.394C>T | p.R132C | RefSeq | GRCh38/hg38 |
NM_001282386 | chr2:g.208248389G>A | c.394C>T | p.R132C | RefSeq | GRCh38/hg38 |
NM_001282386.1 | chr2:g.208248389G>A | c.394C>T | p.R132C | RefSeq | GRCh38/hg38 |
NM_005896.3 | chr2:g.208248389G>A | c.394C>T | p.R132C | RefSeq | GRCh38/hg38 |
NM_005896 | chr2:g.208248389G>A | c.394C>T | p.R132C | RefSeq | GRCh38/hg38 |
NM_005896.4 | chr2:g.208248389G>A | c.394C>T | p.R132C | RefSeq | GRCh38/hg38 |
NM_001282387 | chr2:g.208248389G>A | c.394C>T | p.R132C | RefSeq | GRCh38/hg38 |
NM_001282387.1 | chr2:g.208248389G>A | c.394C>T | p.R132C | RefSeq | GRCh38/hg38 |
NM_001282387.1 | chr2:g.208248389G>A | c.394C>T | p.R132C | RefSeq | GRCh38/hg38 |
Molecular Profile | Protein Effect | Treatment Approaches |
---|---|---|
IDH1 R132C | gain of function | IDH Inhibitor (Pan) IDH1 Inhibitor |
IDH1 R132C IDH1 S280F | ||
IDH1 R132C IDH2 R172K | ||
IDH1 R132C IDH1 D279N | ||
IDH1 R132C IDH1 D279N IDH2 R140Q | ||
IDH1 G131A IDH1 R132C | ||
IDH1 R132C IDH1 D279N IDH1 H315D | ||
IDH1 R132C IDH2 R140Q | ||
IDH1 R132C IDH1 T313I | ||
BRAF V600E IDH1 R132C |