Missing content? – Request curation!
Request curation for specific Genes, Variants, or PubMed publications.
Have questions, comments, or suggestions? - Let us know!
Email us at : ckbsupport@genomenon.com
Gene | IDH1 |
Variant | R132L |
Impact List | missense |
Protein Effect | gain of function |
Gene Variant Descriptions | IDH1 R132L lies within the active site of the Idh1 protein (PMID: 19228619). R132L confers a gain of function to Idh1, as indicated by increased conversion of alpha-ketoglutarate to the onco-metabolite 2HG (R(-)-2-hydroxyglutarate) in cell culture (PMID: 19935646, PMID: 21326614). |
Associated Drug Resistance | |
Category Variants Paths |
IDH1 mutant IDH1 act mut IDH1 R132L IDH1 mutant IDH1 R132X IDH1 R132L |
Transcript | NM_005896.4 |
gDNA | chr2:g.208248388C>A |
cDNA | c.395G>T |
Protein | p.R132L |
Source Database | RefSeq |
Genome Build | GRCh38/hg38 |
Transcript | gDNA | cDNA | Protein | Source Database | Genome Build |
---|---|---|---|---|---|
NM_005896 | chr2:g.208248388C>A | c.395G>T | p.R132L | RefSeq | GRCh38/hg38 |
NM_001282386.1 | chr2:g.208248388C>A | c.395G>T | p.R132L | RefSeq | GRCh38/hg38 |
NM_005896.3 | chr2:g.208248388C>A | c.395G>T | p.R132L | RefSeq | GRCh38/hg38 |
NM_001282386.1 | chr2:g.208248388C>A | c.395G>T | p.R132L | RefSeq | GRCh38/hg38 |
NM_005896.4 | chr2:g.208248388C>A | c.395G>T | p.R132L | RefSeq | GRCh38/hg38 |
NM_001282386 | chr2:g.208248388C>A | c.395G>T | p.R132L | RefSeq | GRCh38/hg38 |
NM_001282387.1 | chr2:g.208248388C>A | c.395G>T | p.R132L | RefSeq | GRCh38/hg38 |
NM_001282387 | chr2:g.208248388C>A | c.395G>T | p.R132L | RefSeq | GRCh38/hg38 |
NM_001282387.1 | chr2:g.208248388C>A | c.395G>T | p.R132L | RefSeq | GRCh38/hg38 |
Molecular Profile | Protein Effect | Treatment Approaches |
---|---|---|
IDH1 R132L | gain of function | IDH Inhibitor (Pan) IDH1 Inhibitor |
IDH1 R119P IDH1 R132L IDH2 R140Q | ||
IDH1 R132L IDH2 R140Q | ||
IDH1 R119P IDH1 R132L | ||
ARID1B Q127_Q131del IDH1 R132L |