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Gene | PIK3CA |
Variant | H1047X |
Impact List | missense |
Protein Effect | unknown |
Gene Variant Descriptions | PIK3CA H1047X indicates any Pik3ca missense mutation that results in the replacement of the histidine (H) at amino acid 1047 by a different amino acid. PIK3CA H1047X mutations are hotspot mutations that may result in increased Pik3ca kinase activity and cell transformation in culture (PMID: 15930273). |
Associated Drug Resistance | |
Category Variants Paths |
PIK3CA mutant PIK3CA exon21 PIK3CA H1047X |
Transcript | NM_006218.4 |
gDNA | chr3:g.179234296_179234298 |
cDNA | c.3139_3141 |
Protein | p.H1047 |
Source Database | RefSeq |
Genome Build | GRCh38/hg38 |
Transcript | gDNA | cDNA | Protein | Source Database | Genome Build |
---|---|---|---|---|---|
XM_006713658.4 | chr3:g.179234296_179234298 | c.3139_3141 | p.H1047 | RefSeq | GRCh38/hg38 |
XM_011512894.2 | chr3:g.179234296_179234298 | c.3139_3141 | p.H1047 | RefSeq | GRCh38/hg38 |
NM_006218 | chr3:g.179234296_179234298 | c.3139_3141 | p.H1047 | RefSeq | GRCh38/hg38 |
NM_006218.4 | chr3:g.179234296_179234298 | c.3139_3141 | p.H1047 | RefSeq | GRCh38/hg38 |
XM_006713658.5 | chr3:g.179234296_179234298 | c.3139_3141 | p.H1047 | RefSeq | GRCh38/hg38 |
XM_011512894 | chr3:g.179234296_179234298 | c.3139_3141 | p.H1047 | RefSeq | GRCh38/hg38 |
XM_006713658 | chr3:g.179234296_179234298 | c.3139_3141 | p.H1047 | RefSeq | GRCh38/hg38 |
NM_006218.3 | chr3:g.179234296_179234298 | c.3139_3141 | p.H1047 | RefSeq | GRCh38/hg38 |
Molecular Profile | Indication/Tumor Type | Response Type | Therapy Name | Approval Status | Evidence Type | Efficacy Evidence | References |
---|---|---|---|---|---|---|---|
PIK3CA H1047X | endometrial adenocarcinoma | predicted - sensitive | Temsirolimus | Case Reports/Case Series | Actionable | In a clinical study, a patient with endometrial adenocarcinoma harboring a PIK3CA H1047 mutation demonstrated a partial response when treated with Torisel (temsirolimus) (PMID: 21216929). | 21216929 |
PIK3CA H1047X | endometrial adenocarcinoma | no benefit | Copanlisib | Case Reports/Case Series | Actionable | In a Phase II (NRG-GY008) trial, Aliqopa (copanlisib) was well tolerated but demonstrated limited efficacy, resulted in progressive disease in a patient with endometrioid adenocarcinoma harboring a PIK3CA H1047 mutation (PMID: 31934607). | 31934607 |
PIK3CA H1047X | endometrial mixed adenocarcinoma | no benefit | Copanlisib | Case Reports/Case Series | Actionable | In a Phase II (NRG-GY008) trial, Aliqopa (copanlisib) was well tolerated but demonstrated limited efficacy, resulted in progressive disease in a patient with endometrial mixed adenocarcinoma harboring a PIK3CA H1047 mutation (PMID: 31934607). | 31934607 |
PIK3CA H1047X | lung non-small cell carcinoma | sensitive | Taselisib | Phase I | Actionable | In a Phase I trial, a non-small cell lung carcinoma patient harboring a mutation at PIK3CA H1047 demonstrated a confirmed partial response when treated with Taselisib (GDC-0032) (PMID: 28331003). | 28331003 |
PIK3CA H1047X | colorectal cancer | predicted - resistant | Bevacizumab + Temsirolimus | Case Reports/Case Series | Actionable | In a clinical study, a colorectal cancer patient harboring a mutation at PIK3CA H1047 demonstrated progressive disease when treated with Torisel (temsirolimus) and Avastin (bevacizumab) (PMID: 21216929). | 21216929 |
PIK3CA H1047X | small intestine adenocarcinoma | predicted - resistant | Bortezomib + Temsirolimus + Topotecan | Case Reports/Case Series | Actionable | In a clinical study, the combination of Torisel (temsirolimus) plus Velcade (bortezomib) and Hycamtin (topotecan) resulted in progressive disease in a patient with small intestine adenocarcinoma harboring a PIK3CA H1047 mutation (PMID: 21216929). | 21216929 |