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Gene | KIT |
Variant | N505I |
Impact List | missense |
Protein Effect | gain of function |
Gene Variant Descriptions | KIT N505I lies within the Ig-like C2-type domain 5 (exon 9) of the Kit protein (UniProt.org). N505I results in constitutive phosphorylation of Kit, activation of downstream Akt and Erk, and is transforming in cell culture (PMID: 24317392). |
Associated Drug Resistance | |
Category Variants Paths |
KIT mutant KIT act mut KIT N505I KIT mutant KIT exon9 KIT N505I |
Transcript | NM_000222.3 |
gDNA | chr4:g.54726024A>T |
cDNA | c.1514A>T |
Protein | p.N505I |
Source Database | RefSeq |
Genome Build | GRCh38/hg38 |
Transcript | gDNA | cDNA | Protein | Source Database | Genome Build |
---|---|---|---|---|---|
NM_000222.2 | chr4:g.54726024A>T | c.1514A>T | p.N505I | RefSeq | GRCh38/hg38 |
NM_000222 | chr4:g.54726024A>T | c.1514A>T | p.N505I | RefSeq | GRCh38/hg38 |
NM_001093772 | chr4:g.54726024A>T | c.1514A>T | p.N505I | RefSeq | GRCh38/hg38 |
NM_001385286.1 | chr4:g.54726024A>T | c.1514A>T | p.N505I | RefSeq | GRCh38/hg38 |
NM_001385285.1 | chr4:g.54726024A>T | c.1514A>T | p.N505I | RefSeq | GRCh38/hg38 |
XM_017008178 | chr4:g.54726024A>T | c.1514A>T | p.N505I | RefSeq | GRCh38/hg38 |
NM_001093772.1 | chr4:g.54726024A>T | c.1514A>T | p.N505I | RefSeq | GRCh38/hg38 |
XM_017008180.1 | chr4:g.54726024A>T | c.1514A>T | p.N505I | RefSeq | GRCh38/hg38 |
XM_017008180 | chr4:g.54726024A>T | c.1514A>T | p.N505I | RefSeq | GRCh38/hg38 |
NM_000222.3 | chr4:g.54726024A>T | c.1514A>T | p.N505I | RefSeq | GRCh38/hg38 |
XM_017008178.1 | chr4:g.54726024A>T | c.1514A>T | p.N505I | RefSeq | GRCh38/hg38 |
NM_001093772.2 | chr4:g.54726024A>T | c.1514A>T | p.N505I | RefSeq | GRCh38/hg38 |
Molecular Profile | Indication/Tumor Type | Response Type | Therapy Name | Approval Status | Evidence Type | Efficacy Evidence | References |
---|---|---|---|---|---|---|---|
KIT N505I | melanoma | predicted - sensitive | Imatinib | Preclinical | Actionable | In a preclinical study, Gleevec (imatinib) decreased phosphorylation of KIT, AKT, and ERK in melanocytes expressing KIT N505I in culture (PMID: 24317392). | 24317392 |
KIT N505I | melanoma | sensitive | Sorafenib | Preclinical | Actionable | In a preclinical study, KIT N505I induced phosphorylation of KIT, ERK, and AKT, and was inhibited by Nexavar (sorafenib) in cell culture of melanocytes, demonstrating sensitivity of N505I to sorafenib (PMID: 24317392). | 24317392 |