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Gene | IDH2 |
Variant | R172X |
Impact List | missense |
Protein Effect | unknown |
Gene Variant Descriptions | IDH2 R172X indicates any Idh2 missense mutation that results in the replacement of the arginine (R) at amino acid 172 by a different amino acid. R172 variants are hotspot mutations in Idh2, which may confer a gain of function to Idh2 resulting in conversion of alpha-ketoglutarate to the onco-metabolite 2HG (R(-)-2-hydroxyglutarate) (PMID: 28711227, PMID: 21326614, PMID: 25495392). |
Associated Drug Resistance | |
Category Variants Paths |
IDH2 mutant IDH2 R172X |
Transcript | NM_002168.4 |
gDNA | chr15:g.90088605_90088607 |
cDNA | c.514_516 |
Protein | p.R172 |
Source Database | RefSeq |
Genome Build | GRCh38/hg38 |
Transcript | gDNA | cDNA | Protein | Source Database | Genome Build |
---|---|---|---|---|---|
NM_002168.4 | chr15:g.90088605_90088607 | c.514_516 | p.R172 | RefSeq | GRCh38/hg38 |
NM_002168 | chr15:g.90088605_90088607 | c.514_516 | p.R172 | RefSeq | GRCh38/hg38 |
NM_002168.3 | chr15:g.90088605_90088607 | c.514_516 | p.R172 | RefSeq | GRCh38/hg38 |
Molecular Profile | Protein Effect | Treatment Approaches |
---|---|---|
IDH2 R172X | unknown | IDH Inhibitor (Pan) IDH2 Inhibitor |