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Gene | VHL |
Variant | D121G |
Impact List | missense |
Protein Effect | loss of function - predicted |
Gene Variant Descriptions | VHL D121G lies within the CCT complex-binding region of the Vhl protein (UniProt.org). D121G retains interaction with Cul2, Roc1, Elongin B, and Hif1/2 in culture (PMID: 11865071, PMID: 17967880, PMID: 19030229), however, results in decreased binding to Elongin C (PMID: 19030229, PMID: 11865071) and impaired Vhl nuclear export and degradation of Hif2a in culture (PMID: 17967880), and therefore, is predicted to lead to a loss of Vhl protein function. |
Associated Drug Resistance | |
Category Variants Paths |
VHL mutant VHL inact mut VHL D121G |
Transcript | NM_000551.4 |
gDNA | chr3:g.10146535A>G |
cDNA | c.362A>G |
Protein | p.D121G |
Source Database | RefSeq |
Genome Build | GRCh38/hg38 |
Transcript | gDNA | cDNA | Protein | Source Database | Genome Build |
---|---|---|---|---|---|
NM_000551.3 | chr3:g.10146535A>G | c.362A>G | p.D121G | RefSeq | GRCh38/hg38 |
NM_000551.4 | chr3:g.10146535A>G | c.362A>G | p.D121G | RefSeq | GRCh38/hg38 |
NM_000551 | chr3:g.10146535A>G | c.362A>G | p.D121G | RefSeq | GRCh38/hg38 |
Molecular Profile | Protein Effect | Treatment Approaches |
---|---|---|
VHL D121G | loss of function - predicted |