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Gene | B2M |
Variant | S14fs |
Impact List | frameshift |
Protein Effect | loss of function |
Gene Variant Descriptions | B2M S14fs results in a change in the amino acid sequence of the B2m protein beginning at aa 14 of 119, likely resulting in premature truncation of the functional protein (UniProt.org). S14fs confers a loss of function to the B2m protein as demonstrated by lack of MHC class I membrane localization (PMID: 27433843, PMID: 29070816). |
Associated Drug Resistance | Y |
Category Variants Paths |
B2M mutant B2M inact mut B2M S14fs |
Transcript | NM_004048.4 |
gDNA | chr15:g.(44711585_44711586) |
cDNA | c.(40_39) |
Protein | p.S14fs |
Source Database | RefSeq |
Genome Build | GRCh38/hg38 |
Transcript | gDNA | cDNA | Protein | Source Database | Genome Build |
---|---|---|---|---|---|
NM_004048.2 | chr15:g.(44711585_44711586) | c.(40_39) | p.S14fs | RefSeq | GRCh38/hg38 |
XM_005254549 | chr15:g.(44711585_44711586) | c.(40_39) | p.S14fs | RefSeq | GRCh38/hg38 |
NM_004048.4 | chr15:g.(44711585_44711586) | c.(40_39) | p.S14fs | RefSeq | GRCh38/hg38 |
XM_005254549.4 | chr15:g.(44711585_44711586) | c.(40_39) | p.S14fs | RefSeq | GRCh38/hg38 |
NM_004048 | chr15:g.(44711585_44711586) | c.(40_39) | p.S14fs | RefSeq | GRCh38/hg38 |
XM_005254549.3 | chr15:g.(44711585_44711586) | c.(40_39) | p.S14fs | RefSeq | GRCh38/hg38 |
Molecular Profile | Indication/Tumor Type | Response Type | Therapy Name | Approval Status | Evidence Type | Efficacy Evidence | References |
---|---|---|---|---|---|---|---|
B2M S14fs | melanoma | predicted - resistant | Pembrolizumab | Case Reports/Case Series | Actionable | In a clinical study, a melanoma patient treated with Keytruda (pembrolizumab) initially demonstrated a partial response, however, post 453 days, developed disease progression likely due to the secondary resistance mutation, B2M S14fs (PMID: 27433843). | 27433843 |