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Gene | POLE |
Variant | A456P |
Impact List | missense |
Protein Effect | unknown |
Gene Variant Descriptions | POLE A456P lies within the exonuclease domain of the Pole protein (PMID: 29352080). A456P has been identified in the scientific literature (PMID: 31829442, PMID: 31624068, PMID: 34910396), but has not been biochemically characterized, and therefore, its effect on Pole protein function is unknown (PubMed, Jun 2024). |
Associated Drug Resistance | |
Category Variants Paths |
POLE mutant POLE A456P |
Transcript | NM_006231.4 |
gDNA | chr12:g.132673271C>G |
cDNA | c.1366G>C |
Protein | p.A456P |
Source Database | RefSeq |
Genome Build | GRCh38/hg38 |
Transcript | gDNA | cDNA | Protein | Source Database | Genome Build |
---|---|---|---|---|---|
XM_011534799 | chr12:g.132673271C>G | c.1366G>C | p.A456P | RefSeq | GRCh38/hg38 |
XM_011534795.3 | chr12:g.132673271C>G | c.1366G>C | p.A456P | RefSeq | GRCh38/hg38 |
NM_006231 | chr12:g.132673271C>G | c.1366G>C | p.A456P | RefSeq | GRCh38/hg38 |
XM_011534802.4 | chr12:g.132643473C>G | c.1366G>C | p.A456P | RefSeq | GRCh38/hg38 |
NM_006231.3 | chr12:g.132673271C>G | c.1366G>C | p.A456P | RefSeq | GRCh38/hg38 |
NM_006231.4 | chr12:g.132673271C>G | c.1366G>C | p.A456P | RefSeq | GRCh38/hg38 |
XM_011534802.3 | chr12:g.132643473C>G | c.1366G>C | p.A456P | RefSeq | GRCh38/hg38 |
XM_047429018.1 | chr12:g.132673271C>G | c.1366G>C | p.A456P | RefSeq | GRCh38/hg38 |
XM_011534802 | chr12:g.132643473C>G | c.1366G>C | p.A456P | RefSeq | GRCh38/hg38 |
XM_011534795.4 | chr12:g.132673271C>G | c.1366G>C | p.A456P | RefSeq | GRCh38/hg38 |
XM_011534795 | chr12:g.132673271C>G | c.1366G>C | p.A456P | RefSeq | GRCh38/hg38 |
XM_011534800 | chr12:g.132673271C>G | c.1366G>C | p.A456P | RefSeq | GRCh38/hg38 |
XM_011534799.2 | chr12:g.132673271C>G | c.1366G>C | p.A456P | RefSeq | GRCh38/hg38 |
XM_011534799.3 | chr12:g.132673271C>G | c.1366G>C | p.A456P | RefSeq | GRCh38/hg38 |
Molecular Profile | Indication/Tumor Type | Response Type | Therapy Name | Approval Status | Evidence Type | Efficacy Evidence | References |
---|---|---|---|---|---|---|---|
POLE A456P | colorectal cancer | predicted - sensitive | Ipilimumab + Nivolumab | Case Reports/Case Series | Actionable | In a retrospective study, treatment with immune checkpoint inhibitors resulted in an overall response rate of 89% (22/29) and a disease control rate of 92% in metastatic colorectal cancer patients harboring pathogenic POLE/POLD1 variants, including a partial response in a patient harboring POLE A456P treated with the combination of Yervoy (ipilimumab) and Opdivo (nivolumab) (PMID: 38777726). | 38777726 |
POLE A456P | colorectal cancer | predicted - sensitive | Pembrolizumab | Case Reports/Case Series | Actionable | In a retrospective study, treatment with immune checkpoint inhibitors resulted in an overall response rate of 89% (22/29) and a disease control rate of 92% in metastatic colorectal cancer patients harboring pathogenic POLE/POLD1 variants, including a partial response in a patient harboring POLE A456P treated with Keytruda (pembrolizumab) (PMID: 38777726). | 38777726 |