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Gene | VHL |
Variant | L158S |
Impact List | missense |
Protein Effect | loss of function |
Gene Variant Descriptions | VHL L158S lies within the Elongin BC complex-interacting region of the Vhl protein (UniProt.org). L158S confers a loss of function to the Vhl protein as demonstrated by decreased interaction with Elongin B/C and Cul2, decreased inhibition of Glut1 and Vegf expression under normoxic conditions (PMID: 9447969), and increased Hif2a, Glut1, Junb, and Egln3 levels in cultured cells (PMID: 16098468). |
Associated Drug Resistance | |
Category Variants Paths |
VHL mutant VHL inact mut VHL L158S |
Transcript | NM_000551.4 |
gDNA | chr3:g.10149795_10149796delCTinsTC |
cDNA | c.472_473delCTinsTC |
Protein | p.L158S |
Source Database | RefSeq |
Genome Build | GRCh38/hg38 |
Transcript | gDNA | cDNA | Protein | Source Database | Genome Build |
---|---|---|---|---|---|
NM_000551.4 | chr3:g.10149795_10149796delCTinsTC | c.472_473delCTinsTC | p.L158S | RefSeq | GRCh38/hg38 |
NM_000551.3 | chr3:g.10149795_10149796delCTinsTC | c.472_473delCTinsTC | p.L158S | RefSeq | GRCh38/hg38 |
NM_000551 | chr3:g.10149795_10149796delCTinsTC | c.472_473delCTinsTC | p.L158S | RefSeq | GRCh38/hg38 |
Molecular Profile | Indication/Tumor Type | Response Type | Therapy Name | Approval Status | Evidence Type | Efficacy Evidence | References |
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