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Gene | VHL |
Variant | Y112N |
Impact List | missense |
Protein Effect | loss of function |
Gene Variant Descriptions | VHL Y112N lies within the CCT complex-binding region of the Vhl protein (UniProt.org). Y112N confers a loss of function to the Vhl protein as demonstrated by reduced stability of the Vhl-Elongin B/C complex (PMID: 16261165), decreased Hif1a ubiquitination in in vitro assays (PMID: 16261165, PMID: 16407835), elevated Hif2a, Glut1, and cyclin D1 expression in normoxic conditions (PMID: 16407835, PMID: 17526729), increased cell proliferation in low serum conditions in culture (PMID: 17526729), and promotion of tumor formation in animal models (PMID: 17526729). |
Associated Drug Resistance | |
Category Variants Paths |
VHL mutant VHL inact mut VHL Y112N |
Transcript | NM_000551.4 |
gDNA | chr3:g.10142181T>A |
cDNA | c.334T>A |
Protein | p.Y112N |
Source Database | RefSeq |
Genome Build | GRCh38/hg38 |
Transcript | gDNA | cDNA | Protein | Source Database | Genome Build |
---|---|---|---|---|---|
NM_000551.3 | chr3:g.10142181T>A | c.334T>A | p.Y112N | RefSeq | GRCh38/hg38 |
NM_198156 | chr3:g.10142181T>A | c.334T>A | p.Y112N | RefSeq | GRCh38/hg38 |
NM_001354723.2 | chr3:g.10142181T>A | c.334T>A | p.Y112N | RefSeq | GRCh38/hg38 |
NM_000551.4 | chr3:g.10142181T>A | c.334T>A | p.Y112N | RefSeq | GRCh38/hg38 |
NM_000551 | chr3:g.10142181T>A | c.334T>A | p.Y112N | RefSeq | GRCh38/hg38 |
NM_001354723.1 | chr3:g.10142181T>A | c.334T>A | p.Y112N | RefSeq | GRCh38/hg38 |
NM_198156.3 | chr3:g.10142181T>A | c.334T>A | p.Y112N | RefSeq | GRCh38/hg38 |
NM_198156.2 | chr3:g.10142181T>A | c.334T>A | p.Y112N | RefSeq | GRCh38/hg38 |
Molecular Profile | Indication/Tumor Type | Response Type | Therapy Name | Approval Status | Evidence Type | Efficacy Evidence | References |
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