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Gene | TSC2 |
Variant | L1597Rfs*4 |
Impact List | frameshift |
Protein Effect | loss of function - predicted |
Gene Variant Descriptions | TSC2 L1597Rfs*4 indicates a shift in the reading frame starting at amino acid 1597 and terminating 4 residues downstream causing a premature truncation of the 1807 amino acid Tsc2 protein (UniProt.org). L1597Rfs*4 has not been characterized however, due to the effects of other truncation mutations downstream of L1597 (PMID: 22903760), is predicted to lead to a loss of Tsc2 protein function. |
Associated Drug Resistance | |
Category Variants Paths |
TSC2 mutant TSC2 inact mut TSC2 L1597Rfs*4 |
Transcript | NM_000548.5 |
gDNA | chr16:g.2086319_2086320insGCCCCCCATAA |
cDNA | c.4789_4790insGCCCCCCATAA |
Protein | p.L1597Rfs*4 |
Source Database | RefSeq |
Genome Build | GRCh38/hg38 |
Transcript | gDNA | cDNA | Protein | Source Database | Genome Build |
---|---|---|---|---|---|
NM_001370404.1 | chr16:g.2086803_2086804insGCCCCCCATAA | c.4789_4790insGCCCCCCATAA | p.L1597Rfs*4 | RefSeq | GRCh38/hg38 |
NM_000548.4 | chr16:g.2086319_2086320insGCCCCCCATAA | c.4789_4790insGCCCCCCATAA | p.L1597Rfs*4 | RefSeq | GRCh38/hg38 |
NM_000548.5 | chr16:g.2086319_2086320insGCCCCCCATAA | c.4789_4790insGCCCCCCATAA | p.L1597Rfs*4 | RefSeq | GRCh38/hg38 |
Molecular Profile | Protein Effect | Treatment Approaches |
---|---|---|
TSC2 L1597Rfs*4 | loss of function - predicted | mTOR Inhibitor mTORC1 Inhibitor |