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Gene | TP53 |
Variant | R280M |
Impact List | missense |
Protein Effect | loss of function |
Gene Variant Descriptions | TP53 R280M lies within the DNA binding domain of the Tp53 protein (UniProt.org). R280M results in decreased DNA binding and activation of Tp53 target genes and resistance to apoptosis in cell culture (PMID: 21643018). |
Associated Drug Resistance | |
Category Variants Paths |
TP53 mutant TP53 exon8 TP53 R280M TP53 mutant TP53 inact mut TP53 R280M |
Transcript | NM_000546.6 |
gDNA | chr17:g.7673780_7673781delGAinsTG |
cDNA | c.839_840delGAinsTG |
Protein | p.R280M |
Source Database | RefSeq |
Genome Build | GRCh38/hg38 |
Transcript | gDNA | cDNA | Protein | Source Database | Genome Build |
---|---|---|---|---|---|
NM_001126113 | chr17:g.7673780_7673781delTCinsCA | c.839_840delGAinsTG | p.R280M | RefSeq | GRCh38/hg38 |
NM_001126113.3 | chr17:g.7673780_7673781delGAinsTG | c.839_840delGAinsTG | p.R280M | RefSeq | GRCh38/hg38 |
NM_000546 | chr17:g.7673780_7673781delTCinsCA | c.839_840delGAinsTG | p.R280M | RefSeq | GRCh38/hg38 |
NM_000546.6 | chr17:g.7673780_7673781delGAinsTG | c.839_840delGAinsTG | p.R280M | RefSeq | GRCh38/hg38 |
NM_001407262.1 | chr17:g.7673780_7673781delGAinsTG | c.839_840delGAinsTG | p.R280M | RefSeq | GRCh38/hg38 |
NM_001126113.2 | chr17:g.7673780_7673781delGAinsTG | c.839_840delGAinsTG | p.R280M | RefSeq | GRCh38/hg38 |
NM_001126114.2 | chr17:g.7673780_7673781delGAinsTG | c.839_840delGAinsTG | p.R280M | RefSeq | GRCh38/hg38 |
NM_001126112 | chr17:g.7673780_7673781delTCinsCA | c.839_840delGAinsTG | p.R280M | RefSeq | GRCh38/hg38 |
NM_001407268.1 | chr17:g.7673780_7673781delGAinsTG | c.839_840delGAinsTG | p.R280M | RefSeq | GRCh38/hg38 |
NM_001407270.1 | chr17:g.7673780_7673781delGAinsTG | c.839_840delGAinsTG | p.R280M | RefSeq | GRCh38/hg38 |
NM_001126114 | chr17:g.7673780_7673781delTCinsCA | c.839_840delGAinsTG | p.R280M | RefSeq | GRCh38/hg38 |
NM_001407266.1 | chr17:g.7673780_7673781delGAinsTG | c.839_840delGAinsTG | p.R280M | RefSeq | GRCh38/hg38 |
NM_001126112.2 | chr17:g.7673780_7673781delGAinsTG | c.839_840delGAinsTG | p.R280M | RefSeq | GRCh38/hg38 |
NM_001407264.1 | chr17:g.7673780_7673781delGAinsTG | c.839_840delGAinsTG | p.R280M | RefSeq | GRCh38/hg38 |
NM_001126114.3 | chr17:g.7673780_7673781delGAinsTG | c.839_840delGAinsTG | p.R280M | RefSeq | GRCh38/hg38 |
NM_000546.5 | chr17:g.7673780_7673781delGAinsTG | c.839_840delGAinsTG | p.R280M | RefSeq | GRCh38/hg38 |
NM_001126112.3 | chr17:g.7673780_7673781delGAinsTG | c.839_840delGAinsTG | p.R280M | RefSeq | GRCh38/hg38 |
Molecular Profile | Indication/Tumor Type | Response Type | Therapy Name | Approval Status | Evidence Type | Efficacy Evidence | References |
---|---|---|---|---|---|---|---|
TP53 R280M | osteosarcoma | resistant | Nutlin-3a | Preclinical | Actionable | In a preclinical study, TP53 R280M resulted in secondary resistance in an osteosarcoma cell line acquired during Nutlin-3 treatment (PMID: 21643018). | 21643018 |