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Gene | KIT |
Variant | V559_T574del |
Impact List | deletion |
Protein Effect | gain of function - predicted |
Gene Variant Descriptions | KIT V559_T574del results in the deletion of 16 amino acids in the juxtamembrane domain (exon 11) of the Kit protein from amino acids 559 to 574 (PMID: 16226710). V559_T574del has not been characterized, however similar Kit exon 11 deletions are activating (PMID: 9438854, PMID: 15365079), and therefore, is predicted to lead to a gain of Kit protein function. |
Associated Drug Resistance | |
Category Variants Paths |
KIT mutant KIT act mut KIT exon 11 del KIT V559_T574del KIT mutant KIT exon11 KIT exon 11 del KIT V559_T574del |
Transcript | NM_000222.3 |
gDNA | chr4:g.54727443_54727490del48 |
cDNA | c.1675_1722del48 |
Protein | p.V559_T574del16 |
Source Database | RefSeq |
Genome Build | GRCh38/hg38 |
Transcript | gDNA | cDNA | Protein | Source Database | Genome Build |
---|---|---|---|---|---|
XM_005265740.1 | chr4:g.54727441_54727488del48 | c.1676_1723del48 | p.K559_P574del16 | RefSeq | GRCh38/hg38 |
XM_017008180 | chr4:g.54727455_54727502del48 | c.1675_1722del48 | p.I559_Y574del16 | RefSeq | GRCh38/hg38 |
XM_005265741 | chr4:g.54727441_54727488del48 | c.1676_1723del48 | p.K559_P574del16 | RefSeq | GRCh38/hg38 |
NM_001093772.2 | chr4:g.54727455_54727502del48 | c.1675_1722del48 | p.I559_Y574del16 | RefSeq | GRCh38/hg38 |
NM_001385292.1 | chr4:g.54727452_54727499del48 | c.1675_1722del48 | p.E559_P574del16 | RefSeq | GRCh38/hg38 |
NM_000222 | chr4:g.54727443_54727490del48 | c.1675_1722del48 | p.V559_T574del16 | RefSeq | GRCh38/hg38 |
XM_005265741.1 | chr4:g.54727441_54727488del48 | c.1676_1723del48 | p.K559_P574del16 | RefSeq | GRCh38/hg38 |
NM_001385290.1 | chr4:g.54727441_54727488del48 | c.1676_1723del48 | p.K559_P574del16 | RefSeq | GRCh38/hg38 |
XM_005265740 | chr4:g.54727441_54727488del48 | c.1676_1723del48 | p.K559_P574del16 | RefSeq | GRCh38/hg38 |
NM_000222.2 | chr4:g.54727443_54727490del48 | c.1675_1722del48 | p.V559_T574del16 | RefSeq | GRCh38/hg38 |
XM_017008178.1 | chr4:g.54727443_54727490del48 | c.1675_1722del48 | p.V559_T574del16 | RefSeq | GRCh38/hg38 |
NM_001093772 | chr4:g.54727455_54727502del48 | c.1675_1722del48 | p.I559_Y574del16 | RefSeq | GRCh38/hg38 |
XM_017008179.1 | chr4:g.54727452_54727499del48 | c.1675_1722del48 | p.E559_P574del16 | RefSeq | GRCh38/hg38 |
XM_017008180.1 | chr4:g.54727455_54727502del48 | c.1675_1722del48 | p.I559_Y574del16 | RefSeq | GRCh38/hg38 |
NM_001385284.1 | chr4:g.54727441_54727488del48 | c.1676_1723del48 | p.K559_P574del16 | RefSeq | GRCh38/hg38 |
XM_017008179 | chr4:g.54727452_54727499del48 | c.1675_1722del48 | p.E559_P574del16 | RefSeq | GRCh38/hg38 |
XM_005265742.3 | chr4:g.54727452_54727499del48 | c.1675_1722del48 | p.E559_P574del16 | RefSeq | GRCh38/hg38 |
NM_001385288.1 | chr4:g.54727452_54727499del48 | c.1675_1722del48 | p.E559_P574del16 | RefSeq | GRCh38/hg38 |
NM_001093772.1 | chr4:g.54727455_54727502del48 | c.1675_1722del48 | p.I559_Y574del16 | RefSeq | GRCh38/hg38 |
NM_000222.3 | chr4:g.54727443_54727490del48 | c.1675_1722del48 | p.V559_T574del16 | RefSeq | GRCh38/hg38 |
NM_001385285.1 | chr4:g.54727443_54727490del48 | c.1675_1722del48 | p.V559_T574del16 | RefSeq | GRCh38/hg38 |
NM_001385286.1 | chr4:g.54727455_54727502del48 | c.1675_1722del48 | p.I559_Y574del16 | RefSeq | GRCh38/hg38 |
XM_005265742 | chr4:g.54727452_54727499del48 | c.1675_1722del48 | p.E559_P574del16 | RefSeq | GRCh38/hg38 |
XM_017008178 | chr4:g.54727443_54727490del48 | c.1675_1722del48 | p.V559_T574del16 | RefSeq | GRCh38/hg38 |
Molecular Profile | Indication/Tumor Type | Response Type | Therapy Name | Approval Status | Evidence Type | Efficacy Evidence | References |
---|---|---|---|---|---|---|---|
KIT V559_T574del | gastrointestinal stromal tumor | predicted - sensitive | Imatinib | Case Reports/Case Series | Actionable | In a clinical case study, Gleevec (imatinib) treatment led to a partial response in a patient with gastrointestinal stromal tumors harboring KIT V559_T574del, with a progression-free survival of 28 months and an overall survival of 54.9 months (PMID: 18294292). | 18294292 |