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Gene | BRAF |
Variant | K601N |
Impact List | missense |
Protein Effect | gain of function |
Gene Variant Descriptions | BRAF K601N lies within the protein kinase domain of the Braf protein (UniProt.org). K601N confers a gain of function on Braf, as indicated by increased phosphorylation of MEK and ERK in cell in culture (PMID: 24434212) and induction of cell proliferation and cell viability in culture (PMID: 29533785). |
Associated Drug Resistance | |
Category Variants Paths |
BRAF mutant BRAF act mut BRAF K601N BRAF mutant BRAF K601X BRAF K601N |
Transcript | NM_004333.6 |
gDNA | chr7:g.140753332T>G |
cDNA | c.1803A>C |
Protein | p.K601N |
Source Database | RefSeq |
Genome Build | GRCh38/hg38 |
Transcript | gDNA | cDNA | Protein | Source Database | Genome Build |
---|---|---|---|---|---|
XM_005250045 | chr7:g.140753332T>G | c.1803A>C | p.K601N | RefSeq | GRCh38/hg38 |
NM_004333.6 | chr7:g.140753332T>G | c.1803A>C | p.K601N | RefSeq | GRCh38/hg38 |
NM_004333 | chr7:g.140753332T>G | c.1803A>C | p.K601N | RefSeq | GRCh38/hg38 |
NM_001378468.1 | chr7:g.140753332T>G | c.1803A>C | p.K601N | RefSeq | GRCh38/hg38 |
NM_004333.5 | chr7:g.140753332T>G | c.1803A>C | p.K601N | RefSeq | GRCh38/hg38 |
NM_001354609.1 | chr7:g.140753332T>G | c.1803A>C | p.K601N | RefSeq | GRCh38/hg38 |
NM_001378474.1 | chr7:g.140753332T>G | c.1803A>C | p.K601N | RefSeq | GRCh38/hg38 |
NM_001354609.2 | chr7:g.140753332T>G | c.1803A>C | p.K601N | RefSeq | GRCh38/hg38 |
Molecular Profile | Indication/Tumor Type | Response Type | Therapy Name | Approval Status | Evidence Type | Efficacy Evidence | References |
---|---|---|---|---|---|---|---|
BRAF K601N | lung non-small cell carcinoma | no benefit | Vemurafenib | Case Reports/Case Series | Actionable | In a Phase II trial, Zelboraf (vemurafenib) treatment did not result in response in the cohort of 15 non-small cell lung cancer patients with non-V600 BRAF mutations, which included 2 patients harboring BRAF K601N, and enrollment in this cohort was discontinued (PMID: 31959346; NCT02304809). | 31959346 |
BRAF K601N | Advanced Solid Tumor | resistant | Vemurafenib | Preclinical - Cell culture | Actionable | In a preclinical study, Zelboraf (vemurafenib) did not inhibit MEK and ERK activation in transformed cells over expressing the constitutively dimerized BRAF K601N (PMID: 26343582). | 26343582 |
BRAF K601N | chronic lymphocytic leukemia | sensitive | PLX8394 | Preclinical - Cell culture | Actionable | In a preclinical study, PLX8394 treatment inhibited Erk signaling and reduced proliferation of chronic lymphocytic leukemia cells harboring BRAF K601N in culture (PMID: 30559419). | 30559419 |
BRAF K601N | hematologic cancer | sensitive | LY3009120 | Preclinical - Cell culture | Actionable | In a preclinical study, a hematological tumor cell line harboring BRAF K601N demonstrated sensitivity to LY3009120 in culture (PMID: 26732095). | 26732095 |
BRAF K601N | lung non-small cell carcinoma | predicted - sensitive | LTT462 + LXH 254 | Case Reports/Case Series | Actionable | In a Phase Ib trial, LTT462 and LXH 254 combination therapy was well tolerated and resulted in an unconfirmed partial response (PR) in 4% (2/49) and stable disease (SD) in 33% (16/49) of patients with advanced or metastatic KRAS- or BRAF-mutant non-small cell lung cancer, with 1 patient harboring BRAF K601N achieving an unconfirmed PR (Ann Oncol 31 (suppl 4):S881-S882; NCT02974725). | detail... |