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Gene | MSH6 |
Variant | T1219I |
Impact List | missense |
Protein Effect | loss of function |
Gene Variant Descriptions | MSH6 T1219I lies within the ATPase domain of the Msh6 protein (PMID: 17531815). T1219I results in a loss of Msh6 protein function, as indicated by loss of mismatch-induced conformational changes and defective DNA mismatch repair activity in in vitro assays (PMID: 22277660, PMID: 31965077). |
Associated Drug Resistance | |
Category Variants Paths |
MSH6 mutant MSH6 inact mut MSH6 T1219I |
Transcript | NM_000179.3 |
gDNA | chr2:g.47806213C>T |
cDNA | c.3656C>T |
Protein | p.T1219I |
Source Database | RefSeq |
Genome Build | GRCh38/hg38 |
Transcript | gDNA | cDNA | Protein | Source Database | Genome Build |
---|---|---|---|---|---|
NM_000179.2 | chr2:g.47806213C>T | c.3656C>T | p.T1219I | RefSeq | GRCh38/hg38 |
NM_001406796.1 | chr2:g.47806213C>T | c.3656C>T | p.T1219I | RefSeq | GRCh38/hg38 |
NM_000179 | chr2:g.47806213C>T | c.3656C>T | p.T1219I | RefSeq | GRCh38/hg38 |
NM_000179.3 | chr2:g.47806213C>T | c.3656C>T | p.T1219I | RefSeq | GRCh38/hg38 |
NM_001406808.1 | chr2:g.47806213C>T | c.3656C>T | p.T1219I | RefSeq | GRCh38/hg38 |
NM_001406809.1 | chr2:g.47806213C>T | c.3656C>T | p.T1219I | RefSeq | GRCh38/hg38 |
NM_001406800.1 | chr2:g.47806213C>T | c.3656C>T | p.T1219I | RefSeq | GRCh38/hg38 |
XM_024452819.1 | chr2:g.47806213C>T | c.3656C>T | p.T1219I | RefSeq | GRCh38/hg38 |
Molecular Profile | Indication/Tumor Type | Response Type | Therapy Name | Approval Status | Evidence Type | Efficacy Evidence | References |
---|---|---|---|---|---|---|---|
MSH6 T1219I | glioblastoma | resistant | Temozolomide | Preclinical | Actionable | In a preclinical study, glioblastoma cells harboring a MSH6 T1219I mutation were resistant to Temodar (temozolomide) in cell culture (PMID: 19584161). | 19584161 |