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Gene | BRAF |
Variant | V47_D380del |
Impact List | deletion |
Protein Effect | gain of function - predicted |
Gene Variant Descriptions | BRAF V47_D380del results in the deletion of 334 amino acids of the Braf protein from amino acids 47 to 380 (UniProt.org). V47_D380del (reported as internal deletion of exons 2-8) has been associated with resistance to Mek inhibitors in a patient (PMID: 29171936), and is predicted to lead to a gain of Braf protein function due to the deletion of the CR1 autoinhibitory domain and preservation of the protein kinase domain (PMID: 23890088, PMID: 22113612). |
Associated Drug Resistance | Y |
Category Variants Paths |
BRAF mutant BRAF act mut BRAF V47_D380del |
Transcript | NM_004333.6 |
gDNA | chr7:g.140794308_140850212del55905 |
cDNA | c.141_1140+2del55905 |
Protein | p.V47_D380del334 |
Source Database | RefSeq |
Genome Build | GRCh38/hg38 |
Transcript | gDNA | cDNA | Protein | Source Database | Genome Build |
---|---|---|---|---|---|
NM_001378468.1 | chr7:g.140794308_140850212del55905 | c.141_1140+2del55905 | p.V47_D380del334 | RefSeq | GRCh38/hg38 |
NM_004333 | chr7:g.140794308_140850212del55905 | c.141_1140+2del55905 | p.V47_D380del334 | RefSeq | GRCh38/hg38 |
XM_047420766.1 | chr7:g.140785690_140834818del49129 | c.139_1140del49129 | p.L47_R380del334 | RefSeq | GRCh38/hg38 |
XM_047420769.1 | chr7:g.140794308_140850212del55905 | c.141_1140+2del55905 | p.V47_D380del334 | RefSeq | GRCh38/hg38 |
NM_001378471.1 | chr7:g.140794308_140850212del55905 | c.141_1140+2del55905 | p.V47_D380del334 | RefSeq | GRCh38/hg38 |
NM_001374258.1 | chr7:g.140794308_140850212del55905 | c.141_1140+2del55905 | p.V47_D380del334 | RefSeq | GRCh38/hg38 |
NM_004333.5 | chr7:g.140794308_140850212del55905 | c.141_1140+2del55905 | p.V47_D380del334 | RefSeq | GRCh38/hg38 |
XM_047420767.1 | chr7:g.140794308_140850212del55905 | c.141_1140+2del55905 | p.V47_D380del334 | RefSeq | GRCh38/hg38 |
NM_004333.6 | chr7:g.140794308_140850212del55905 | c.141_1140+2del55905 | p.V47_D380del334 | RefSeq | GRCh38/hg38 |
XM_047420768.1 | chr7:g.140794308_140850212del55905 | c.141_1140+2del55905 | p.V47_D380del334 | RefSeq | GRCh38/hg38 |
NM_001378470.1 | chr7:g.140783093_140834872del51780 | c.143_1144del51780 | p.Y48_A381del334 | RefSeq | GRCh38/hg38 |
NM_001378469.1 | chr7:g.140794308_140850212del55905 | c.141_1140+2del55905 | p.V47_D380del334 | RefSeq | GRCh38/hg38 |
XM_017012558 | chr7:g.140794308_140850212del55905 | c.141_1140+2del55905 | p.V47_D380del334 | RefSeq | GRCh38/hg38 |
NM_001374244.1 | chr7:g.140794308_140850212del55905 | c.141_1140+2del55905 | p.V47_D380del334 | RefSeq | GRCh38/hg38 |
XM_017012559 | chr7:g.140794308_140850212del55905 | c.141_1140+2del55905 | p.V47_D380del334 | RefSeq | GRCh38/hg38 |
NM_001378472.1 | chr7:g.140783039_140834818del51780 | c.139_1140del51780 | p.L47_S380del334 | RefSeq | GRCh38/hg38 |
NM_001354609.2 | chr7:g.140794308_140850212del55905 | c.141_1140+2del55905 | p.V47_D380del334 | RefSeq | GRCh38/hg38 |
XM_005250045 | chr7:g.140794308_140850212del55905 | c.141_1140+2del55905 | p.V47_D380del334 | RefSeq | GRCh38/hg38 |
NM_001378474.1 | chr7:g.140794308_140850212del55905 | c.141_1140+2del55905 | p.V47_D380del334 | RefSeq | GRCh38/hg38 |
XM_017012559.1 | chr7:g.140794308_140850212del55905 | c.141_1140+2del55905 | p.V47_D380del334 | RefSeq | GRCh38/hg38 |
NM_001378473.1 | chr7:g.140783039_140834818del51780 | c.139_1140del51780 | p.L47_S380del334 | RefSeq | GRCh38/hg38 |
NM_001378475.1 | chr7:g.140781604_140850212del68609 | c.140_1141del68609 | p.V47_F380del334 | RefSeq | GRCh38/hg38 |
NM_001354609.1 | chr7:g.140794308_140850212del55905 | c.141_1140+2del55905 | p.V47_D380del334 | RefSeq | GRCh38/hg38 |
XM_017012558.1 | chr7:g.140794308_140850212del55905 | c.141_1140+2del55905 | p.V47_D380del334 | RefSeq | GRCh38/hg38 |
XM_047420770.1 | chr7:g.140753281_140800369del47089 | c.140_1141del47089 | p.S47_L380del334 | RefSeq | GRCh38/hg38 |
NM_001378467.1 | chr7:g.140794317_140850212del55896 | c.139_1140del55896 | p.V47_V380del334 | RefSeq | GRCh38/hg38 |
XM_017012559.2 | chr7:g.140794308_140850212del55905 | c.141_1140+2del55905 | p.V47_D380del334 | RefSeq | GRCh38/hg38 |
Molecular Profile | Indication/Tumor Type | Response Type | Therapy Name | Approval Status | Evidence Type | Efficacy Evidence | References |
---|---|---|---|---|---|---|---|
BRAF V47_D380del | melanoma | predicted - resistant | Dabrafenib + Trametinib | Case Reports/Case Series | Actionable | In a clinical case study, a melanoma patient developed progressive disease after initial response to Tafinlar (dabrafenib) and Mekinist (trametinib) combination treatment, BRAF V47_D380del was identified as an acquired mutation in the progressing lesion along with mutations presented in both primary and progressing lesions, including BRAF V600E, PTEN G129E, CDKN2A/B loss, and TERT promoter mutations (PMID: 29171936). | 29171936 |