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Gene | PIK3CA |
Variant | R88Q |
Impact List | missense |
Protein Effect | gain of function |
Gene Variant Descriptions | PIK3CA R88Q lies within the PI3K-ABD domain of the Pik3ca protein (UniProt.org). R88Q confers a gain of function to the Pik3ca protein as indicated by increased phosphorylation of downstream targets Akt and S6, increased cell proliferation and migration, and is transforming in culture (PMID: 18829572, PMID: 29533785, PMID: 34779417). |
Associated Drug Resistance | |
Category Variants Paths |
PIK3CA mutant PIK3CA act mut PIK3CA R88Q |
Transcript | NM_006218.4 |
gDNA | chr3:g.179199088G>A |
cDNA | c.263G>A |
Protein | p.R88Q |
Source Database | RefSeq |
Genome Build | GRCh38/hg38 |
Transcript | gDNA | cDNA | Protein | Source Database | Genome Build |
---|---|---|---|---|---|
XM_011512894 | chr3:g.179199088G>A | c.263G>A | p.R88Q | RefSeq | GRCh38/hg38 |
XM_006713658.5 | chr3:g.179199088G>A | c.263G>A | p.R88Q | RefSeq | GRCh38/hg38 |
NM_006218.4 | chr3:g.179199088G>A | c.263G>A | p.R88Q | RefSeq | GRCh38/hg38 |
NM_006218.3 | chr3:g.179199088G>A | c.263G>A | p.R88Q | RefSeq | GRCh38/hg38 |
XM_011512894.2 | chr3:g.179199088G>A | c.263G>A | p.R88Q | RefSeq | GRCh38/hg38 |
XM_006713658 | chr3:g.179199088G>A | c.263G>A | p.R88Q | RefSeq | GRCh38/hg38 |
XM_006713658.4 | chr3:g.179199088G>A | c.263G>A | p.R88Q | RefSeq | GRCh38/hg38 |
NM_006218 | chr3:g.179199088G>A | c.263G>A | p.R88Q | RefSeq | GRCh38/hg38 |
Molecular Profile | Indication/Tumor Type | Response Type | Therapy Name | Approval Status | Evidence Type | Efficacy Evidence | References |
---|---|---|---|---|---|---|---|
PIK3CA R88Q | colorectal cancer | predicted - sensitive | Cetuximab + Floxuridine + Fluorouracil + Irinotecan | Case Reports/Case Series | Actionable | In a retrospective analysis, treatment with the combination of Erbitux (cetuximab), Adrucil (fluorouracil), Camptosar (irinotecan), and Floxuridine resulted in at least 24 months without evidence of disease in a colorectal carcinoma patient harboring a PIK3CA R88Q mutation (PMID: 25714871). | 25714871 |
PIK3CA R88Q | malignant pleural mesothelioma | predicted - sensitive | Apitolisib | Case Reports/Case Series | Actionable | In a Phase I trial, treatment with Apitolisib (GDC-0980) resulted in a partial response in a patient with malignant pleural mesothelioma harboring PIK3CA R88Q (PMID: 26787751; NCT00854152). | 26787751 |
PIK3CA R88Q | high grade glioma | sensitive | Buparlisib + Selumetinib | Preclinical - Cell culture | Actionable | In a preclinical study, the combination therapy of Buparlisib (BKM120) and Koselugo (selumetinib) led to a synergistic effect, resulting in greater growth inhibition of astrocytoma cells expressing PIK3CA R88Q than cells with wild-type PIK3CA in culture (PMID: 29975751). | 29975751 |
PIK3CA R88Q | tonsil squamous cell carcinoma | predicted - sensitive | Alpelisib + Tipifarnib | Case Reports/Case Series | Actionable | In a Phase I/II trial (KURRENT-HN), the combination of Piqray (alpelisib) and Zarnestra (tipifarnib) resulted in a partial response with an 84% reduction in the target lesions and a complete response in the lung in a patient with metastatic squamous cell carcinoma of the tonsil harboring PIK3CA R88Q, with response ongoing at 27 weeks (PMID: 37339176; NCT04997902). | 37339176 |