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Gene | KIT |
Variant | E554_Y570del |
Impact List | deletion |
Protein Effect | gain of function - predicted |
Gene Variant Descriptions | KIT E554_Y570del results in the deletion of 17 amino acids in the juxtamembrane domain (exon 11) of the Kit protein from amino acids 554 to 570 (PMID: 16226710). E554_Y570del has not been characterized, however similar Kit exon 11 deletions are activating (PMID: 9438854, PMID: 15365079), and therefore, is predicted to lead to a gain of Kit protein function. |
Associated Drug Resistance | |
Category Variants Paths |
KIT mutant KIT act mut KIT exon 11 del KIT E554_Y570del KIT mutant KIT exon11 KIT exon 11 del KIT E554_Y570del |
Transcript | NM_000222.3 |
gDNA | chr4:g.54727428_54727478del51 |
cDNA | c.1660_1710del51 |
Protein | p.E554_Y570del17 |
Source Database | RefSeq |
Genome Build | GRCh38/hg38 |
Transcript | gDNA | cDNA | Protein | Source Database | Genome Build |
---|---|---|---|---|---|
NM_001093772.2 | chr4:g.54727440_54727490del51 | c.1660_1710del51 | p.K554_T570del17 | RefSeq | GRCh38/hg38 |
NM_001385284.1 | chr4:g.54727427_54727477del51 | c.1662_1712del51 | p.E555_Y571del17 | RefSeq | GRCh38/hg38 |
NM_001385285.1 | chr4:g.54727428_54727478del51 | c.1660_1710del51 | p.E554_Y570del17 | RefSeq | GRCh38/hg38 |
NM_001385286.1 | chr4:g.54727440_54727490del51 | c.1660_1710del51 | p.K554_T570del17 | RefSeq | GRCh38/hg38 |
NM_000222.2 | chr4:g.54727428_54727478del51 | c.1660_1710del51 | p.E554_Y570del | RefSeq | GRCh38/hg38 |
NM_001385292.1 | chr4:g.54727437_54727487del51 | c.1660_1710del51 | p.W554_P570del17 | RefSeq | GRCh38/hg38 |
NM_001385288.1 | chr4:g.54727437_54727487del51 | c.1660_1710del51 | p.W554_P570del17 | RefSeq | GRCh38/hg38 |
NM_001385290.1 | chr4:g.54727427_54727477del51 | c.1662_1712del51 | p.E555_Y571del17 | RefSeq | GRCh38/hg38 |
NM_000222.3 | chr4:g.54727428_54727478del51 | c.1660_1710del51 | p.E554_Y570del17 | RefSeq | GRCh38/hg38 |
Molecular Profile | Indication/Tumor Type | Response Type | Therapy Name | Approval Status | Evidence Type | Efficacy Evidence | References |
---|---|---|---|---|---|---|---|
KIT E554_Y570del | gastrointestinal stromal tumor | predicted - sensitive | Imatinib | Case Reports/Case Series | Actionable | In a clinical case study, Gleevec (imatinib) treatment led to a partial response in a patient with gastrointestinal stromal tumor harboring KIT E554_Y570del, with a progression-free survival of 11.5 months and overall survival of 34.1 months (PMID: 18294292). | 18294292 |