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Gene | KIT |
Variant | V555_D572del |
Impact List | deletion |
Protein Effect | gain of function - predicted |
Gene Variant Descriptions | KIT V555_D572del results in the deletion of 18 amino acids in the juxtamembrane domain (exon 11) of the Kit protein from amino acids 555 to 572 (PMID: 16226710). V555_D572del has not been characterized, however similar Kit exon 11 deletions are activating (PMID: 9438854, PMID: 15365079), and therefore, is predicted to lead to a gain of Kit protein function. |
Associated Drug Resistance | |
Category Variants Paths |
KIT mutant KIT act mut KIT exon 11 del KIT V555_D572del KIT mutant KIT exon11 KIT exon 11 del KIT V555_D572del |
Transcript | NM_000222.3 |
gDNA | chr4:g.54727431_54727484del54 |
cDNA | c.1663_1716del54 |
Protein | p.V555_D572del18 |
Source Database | RefSeq |
Genome Build | GRCh38/hg38 |
Transcript | gDNA | cDNA | Protein | Source Database | Genome Build |
---|---|---|---|---|---|
NM_001385284.1 | chr4:g.54727430_54727483del54 | c.1665_1718del54 | p.E555_I572del18 | RefSeq | GRCh38/hg38 |
XM_017008178.1 | chr4:g.54727431_54727484del54 | c.1663_1716del54 | p.V555_D572del | RefSeq | GRCh38/hg38 |
NM_000222.2 | chr4:g.54727431_54727484del54 | c.1663_1716del54 | p.V555_D572del | RefSeq | GRCh38/hg38 |
NM_001385290.1 | chr4:g.54727430_54727483del54 | c.1665_1718del54 | p.E555_I572del18 | RefSeq | GRCh38/hg38 |
NM_001385292.1 | chr4:g.54727440_54727493del54 | c.1663_1716del54 | p.K555_Q572del18 | RefSeq | GRCh38/hg38 |
NM_000222.3 | chr4:g.54727431_54727484del54 | c.1663_1716del54 | p.V555_D572del18 | RefSeq | GRCh38/hg38 |
NM_001385288.1 | chr4:g.54727440_54727493del54 | c.1663_1716del54 | p.K555_Q572del18 | RefSeq | GRCh38/hg38 |
NM_001093772.2 | chr4:g.54727443_54727496del54 | c.1663_1716del54 | p.V555_L572del18 | RefSeq | GRCh38/hg38 |
NM_001385285.1 | chr4:g.54727431_54727484del54 | c.1663_1716del54 | p.V555_D572del18 | RefSeq | GRCh38/hg38 |
NM_001385286.1 | chr4:g.54727443_54727496del54 | c.1663_1716del54 | p.V555_L572del18 | RefSeq | GRCh38/hg38 |
Molecular Profile | Indication/Tumor Type | Response Type | Therapy Name | Approval Status | Evidence Type | Efficacy Evidence | References |
---|---|---|---|---|---|---|---|
KIT V555_D572del | gastrointestinal stromal tumor | predicted - sensitive | Imatinib | Case Reports/Case Series | Actionable | In a clinical case study, Gleevec (imatinib) treatment led to a partial response in a patient with gastrointestinal stromal tumor harboring KIT V555_D572del, with a progression-free survival of 49.4 mo and an overall survival of 59.3 mo (PMID: 18294292). | 18294292 |