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Gene | KIT |
Variant | M1? |
Impact List | unknown |
Protein Effect | unknown |
Gene Variant Descriptions | KIT M1? indicates a disruption of the methionine (M) start codon with an unknown translational effect on the Kit protein. M1? has not been characterized and therefore, its effect on Kit protein function is unknown (PubMed, Oct 2024). |
Associated Drug Resistance | |
Category Variants Paths |
KIT mutant KIT M1? |
Transcript | NM_000222.3 |
gDNA | chr4:g.54658015_54658017 |
cDNA | c.1_3 |
Protein | p.M1 |
Source Database | RefSeq |
Genome Build | GRCh38/hg38 |
Transcript | gDNA | cDNA | Protein | Source Database | Genome Build |
---|---|---|---|---|---|
XM_005265740.1 | chr4:g.54658015_54658017 | c.1_3 | p.M1 | RefSeq | GRCh38/hg38 |
XM_017008179.1 | chr4:g.54658015_54658017 | c.1_3 | p.M1 | RefSeq | GRCh38/hg38 |
NM_000222.3 | chr4:g.54658015_54658017 | c.1_3 | p.M1 | RefSeq | GRCh38/hg38 |
XM_005265741.1 | chr4:g.54658015_54658017 | c.1_3 | p.M1 | RefSeq | GRCh38/hg38 |
NM_001385288.1 | chr4:g.54658015_54658017 | c.1_3 | p.M1 | RefSeq | GRCh38/hg38 |
NM_001093772.2 | chr4:g.54658015_54658017 | c.1_3 | p.M1 | RefSeq | GRCh38/hg38 |
XM_017008178.1 | chr4:g.54658015_54658017 | c.1_3 | p.M1 | RefSeq | GRCh38/hg38 |
NM_001385292.1 | chr4:g.54658015_54658017 | c.1_3 | p.M1 | RefSeq | GRCh38/hg38 |
NM_001385284.1 | chr4:g.54658015_54658017 | c.1_3 | p.M1 | RefSeq | GRCh38/hg38 |
NM_001385286.1 | chr4:g.54658015_54658017 | c.1_3 | p.M1 | RefSeq | GRCh38/hg38 |
XM_005265742.3 | chr4:g.54658015_54658017 | c.1_3 | p.M1 | RefSeq | GRCh38/hg38 |
NM_001385290.1 | chr4:g.54658015_54658017 | c.1_3 | p.M1 | RefSeq | GRCh38/hg38 |
NM_000222.2 | chr4:g.54658015_54658017 | c.1_3 | p.M1 | RefSeq | GRCh38/hg38 |
XM_017008180.1 | chr4:g.54658015_54658017 | c.1_3 | p.M1 | RefSeq | GRCh38/hg38 |
NM_001093772.1 | chr4:g.54658015_54658017 | c.1_3 | p.M1 | RefSeq | GRCh38/hg38 |
NM_001385285.1 | chr4:g.54658015_54658017 | c.1_3 | p.M1 | RefSeq | GRCh38/hg38 |
Molecular Profile | Indication/Tumor Type | Response Type | Therapy Name | Approval Status | Evidence Type | Efficacy Evidence | References |
---|---|---|---|---|---|---|---|
KIT mutant | gastrointestinal stromal tumor | predicted - sensitive | Avapritinib | Phase I | Actionable | In a Phase I (NAVIGATOR) trial, Ayvakit (avapritinib) treatment resulted in an objective response rate of 13% (7/52, 7 partial responses) and a disease control rate of 63% (33/52) in patients with KIT-mutant gastrointestinal stromal tumor (The CTOS 2018 Annual Meeting, Nov 14-17, Rome Italy, Paper 012 3027631; NCT02508532). | detail... |
KIT mutant | gastrointestinal stromal tumor | predicted - sensitive | Ripretinib | Phase I | Actionable | In a Phase I trial, Qinlock (ripretinib) was well tolerated, resulted in an objective response in 11.3% (16/142, 16 partial responses) and stable disease in 61.3% (87/142) of patients with advanced gastrointestinal stromal tumor harboring KIT (exon 11, n=103; exon 9, n=26; other, n=6) or PDGFRA mutations (n=7), with a median progression-free survival of 5.6 months (PMID: 32804590; NCT02571036). | 32804590 |
KIT mutant | gastrointestinal stromal tumor | predicted - sensitive | Ripretinib | Phase I | Actionable | In a Phase I trial, Qinlock (ripretinib) demonstrated preliminary safety and efficacy in patients with advanced solid tumors, including KIT-mutant gastrointestinal stromal tumor (GIST), with 1 patient harboring KIT exon 11 and 17 mutations demonstrating a partial response, and 7/7 KIT-mutant GIST patients demonstrating a partial metabolic response (EORTC-NCI-AACR 2016, Abs 7LBA). | detail... |
KIT mutant | gastrointestinal stromal tumor | not applicable | N/A | Clinical Study | Diagnostic | KIT mutations are used in the diagnosis of gastrointestinal stromal tumors (PMID: 25193432, PMID: 26276366, PMID: 25729899). | 25193432 26276366 25729899 |
KIT mutant | melanoma | predicted - sensitive | Ripretinib | Phase I | Actionable | In a Phase I trial, Qinlock (ripretinib) treatment demonstrated manageable safety and preliminary efficacy in patients with KIT-mutated melanoma, and led to an objective response rate of 23% (6/26, 1 complete and 5 partial responses), a median progression-free survival of 7.3 months, and a median duration of response of 9.1 months (PMID: 35753087; NCT02571036). | 35753087 |
KIT mutant | melanoma | sensitive | Nilotinib | Phase II | Actionable | In a Phase II trial, Tasigna (nilotinib) treatment resulted in complete response in 4% (1/25), durable partial response in 16% (4/25), and stable disease in 56% (14/25) of melanoma patients harboring KIT mutations (PMID: 28843487; NCT01168050). | 28843487 |
KIT mutant | melanoma | sensitive | Nilotinib | Phase II | Actionable | In a Phase II trial, Tasigna (nilotinib) treatment in patients with melanoma harboring KIT mutations resulted in an overall response rate of 26.2% (11/42), which included 11 patients with a partial response, a median duration of response of 7.1 months, and an overall survival of 18 months (PMID: 28327988; NCT01028222). | 28327988 |
KIT mutant | gastrointestinal stromal tumor | sensitive | Imatinib + Infigratinib | Preclinical - Pdx | Actionable | In a preclinical study, Truseltiq (infigratinib) and Gleevec (imatinib) combination treatment demonstrated enhanced antitumor activity in patient derived xenograft models of gastrointestinal stromal tumor harboring KIT mutations (PMID: 25673643). | 25673643 |