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Gene | BRAF |
Variant | L597V |
Impact List | missense |
Protein Effect | gain of function |
Gene Variant Descriptions | BRAF L597V lies within the protein kinase domain of the Braf protein (UniProt.org). L597V results in activation of Braf as indicated by increased phosphorylation of Mek and Erk in cell culture (PMID: 22798288) and and induces cell proliferation and cell viability in culture (PMID: 29533785). |
Associated Drug Resistance | |
Category Variants Paths |
BRAF mutant BRAF act mut BRAF L597V BRAF mutant BRAF L597X BRAF L597V |
Transcript | NM_004333.6 |
gDNA | chr7:g.140753346G>C |
cDNA | c.1789C>G |
Protein | p.L597V |
Source Database | RefSeq |
Genome Build | GRCh38/hg38 |
Transcript | gDNA | cDNA | Protein | Source Database | Genome Build |
---|---|---|---|---|---|
NM_004333.6 | chr7:g.140753346G>C | c.1789C>G | p.L597V | RefSeq | GRCh38/hg38 |
NM_001378472.1 | chr7:g.140749334A>C | c.1789T>G | p.L597V | RefSeq | GRCh38/hg38 |
NM_004333.5 | chr7:g.140753346G>C | c.1789C>G | p.L597V | RefSeq | GRCh38/hg38 |
NM_001354609.2 | chr7:g.140753346G>C | c.1789C>G | p.L597V | RefSeq | GRCh38/hg38 |
NM_001354609.1 | chr7:g.140753346G>C | c.1789C>G | p.L597V | RefSeq | GRCh38/hg38 |
NM_004333 | chr7:g.140753346G>C | c.1789C>G | p.L597V | RefSeq | GRCh38/hg38 |
NM_001378473.1 | chr7:g.140749334A>C | c.1789T>G | p.L597V | RefSeq | GRCh38/hg38 |
NM_001378474.1 | chr7:g.140753346G>C | c.1789C>G | p.L597V | RefSeq | GRCh38/hg38 |
XM_005250045 | chr7:g.140753346G>C | c.1789C>G | p.L597V | RefSeq | GRCh38/hg38 |
NM_001378468.1 | chr7:g.140753346G>C | c.1789C>G | p.L597V | RefSeq | GRCh38/hg38 |
Molecular Profile | Indication/Tumor Type | Response Type | Therapy Name | Approval Status | Evidence Type | Efficacy Evidence | References |
---|---|---|---|---|---|---|---|
BRAF L597V | endometrial adenocarcinoma | no benefit | Trametinib | Case Reports/Case Series | Actionable | In a Phase II trial (NCI-MATCH), Mekinist (trametinib) treatment did not demonstrate clinical activity in patients with advanced solid tumors or lymphoma harboring BRAF fusion or non-V600 mutations, resulted in stable disease with a progression-free survival of 7.9 months in a patient with endometrial adenocarcinoma harboring BRAF L597V (PMID: 31924734; NCT02465060). | 31924734 |
BRAF L597V | lung adenocarcinoma | sensitive | Trametinib | Preclinical - Patient cell culture | Actionable | In a preclinical study, cells derived from a lung adenocarcinoma patient harboring BRAF L597V were sensitive to treatment with Mekinist (trametinib) in culture, demonstrating inhibition of cell growth (PMID: 32540409). | 32540409 |
BRAF L597V | lung adenocarcinoma | resistant | Dabrafenib | Preclinical - Patient cell culture | Actionable | In a preclinical study, cells derived from a lung adenocarcinoma patient harboring BRAF L597V were resistant to treatment with Tafinlar (dabrafenib) in culture (PMID: 32540409). | 32540409 |
BRAF L597V | lung adenocarcinoma | resistant | Vemurafenib | Preclinical - Patient cell culture | Actionable | In a preclinical study, cells derived from a lung adenocarcinoma patient harboring BRAF L597V were resistant to treatment with Zelboraf (vemurafenib) in culture (PMID: 32540409). | 32540409 |
BRAF L597V | Advanced Solid Tumor | resistant | Vemurafenib | Preclinical - Cell culture | Actionable | In a preclinical study, Zelboraf (vemurafenib) did not inhibit MEK and ERK activation in transformed cells over expressing the constitutively dimerized BRAF L597V (PMID: 26343582). | 26343582 |
BRAF L597V | lung adenocarcinoma | resistant | Encorafenib | Preclinical - Patient cell culture | Actionable | In a preclinical study, cells derived from a lung adenocarcinoma patient harboring BRAF L597V were resistant to treatment with Braftovi (encorafenib) in culture (PMID: 32540409). | 32540409 |
BRAF L597V | lung adenocarcinoma | resistant | Ulixertinib | Preclinical - Patient cell culture | Actionable | In a preclinical study, cells derived from a lung adenocarcinoma patient harboring BRAF L597V were resistant to treatment with Ulixertinib (BVD-523) in culture (PMID: 32540409). | 32540409 |
BRAF L597V | lung adenocarcinoma | resistant | Tovorafenib | Preclinical - Patient cell culture | Actionable | In a preclinical study, cells derived from a lung adenocarcinoma patient harboring BRAF L597V were resistant to treatment with Ojemda (tovorafenib) in culture (PMID: 32540409). | 32540409 |
BRAF L597V | lung adenocarcinoma | sensitive | Dabrafenib + Trametinib | Preclinical - Patient cell culture | Actionable | In a preclinical study, cells derived from a lung adenocarcinoma patient harboring BRAF L597V were sensitive to the combination treatment of Tafinlar (dabrafenib) and Mekinist (trametinib) in culture, demonstrating inhibition of cell growth (PMID: 32540409). | 32540409 |
BRAF L597V | lung adenocarcinoma | resistant | Ravoxertinib | Preclinical - Patient cell culture | Actionable | In a preclinical study, cells derived from a lung adenocarcinoma patient harboring BRAF L597V were resistant to treatment with Ravoxertinib (GDC-0994) in culture (PMID: 32540409). | 32540409 |
BRAF L597V | lung adenocarcinoma | resistant | MK-8353 | Preclinical - Patient cell culture | Actionable | In a preclinical study, cells derived from a lung adenocarcinoma patient harboring BRAF L597V were resistant to treatment with MK-8353 in culture (PMID: 32540409). | 32540409 |
BRAF L597V | lung adenocarcinoma | sensitive | Lifirafenib | Preclinical - Patient cell culture | Actionable | In a preclinical study, cells derived from a lung adenocarcinoma patient harboring BRAF L597V were sensitive to treatment with Lifirafenib (BGB-283) in culture, demonstrating inhibition of cell growth (PMID: 32540409). | 32540409 |
BRAF L597V | lung adenocarcinoma | sensitive | LXH 254 | Preclinical - Patient cell culture | Actionable | In a preclinical study, cells derived from a lung adenocarcinoma patient harboring BRAF L597V were sensitive to treatment with LXH 254 in culture, demonstrating inhibition of cell growth (PMID: 32540409). | 32540409 |
BRAF L597V | lung adenocarcinoma | resistant | LY3214996 | Preclinical - Patient cell culture | Actionable | In a preclinical study, cells derived from a lung adenocarcinoma patient harboring BRAF L597V were resistant to treatment with LY3214996 in culture (PMID: 32540409). | 32540409 |