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Gene | TET2 |
Variant | V1199E |
Impact List | missense |
Protein Effect | unknown |
Gene Variant Descriptions | TET2 V1199E lies within the catalytic domain of the Tet2 protein (PMID: 24315485). V1199E has been demonstrated to confer RAF inhibitor resistance in the context of BRAF V600E (PMID: 34433654), but has not been biochemically characterized and therefore, its effect on Tet2 protein function is unknown (PubMed, Nov 2024). |
Associated Drug Resistance | Y |
Category Variants Paths |
TET2 mutant TET2 V1199E |
Transcript | NM_001127208.3 |
gDNA | chr4:g.105243571T>A |
cDNA | c.3596T>A |
Protein | p.V1199E |
Source Database | RefSeq |
Genome Build | GRCh38/hg38 |
Transcript | gDNA | cDNA | Protein | Source Database | Genome Build |
---|---|---|---|---|---|
NM_001127208.3 | chr4:g.105243571T>A | c.3596T>A | p.V1199E | RefSeq | GRCh38/hg38 |
NM_001127208.2 | chr4:g.105243571T>A | c.3596T>A | p.V1199E | RefSeq | GRCh38/hg38 |
XM_024454103.2 | chr4:g.105243571T>A | c.3596T>A | p.V1199E | RefSeq | GRCh38/hg38 |
XM_024454102.1 | chr4:g.105243571T>A | c.3596T>A | p.V1199E | RefSeq | GRCh38/hg38 |
XM_024454103.1 | chr4:g.105243571T>A | c.3596T>A | p.V1199E | RefSeq | GRCh38/hg38 |
XM_005263082.3 | chr4:g.105243571T>A | c.3596T>A | p.V1199E | RefSeq | GRCh38/hg38 |
XM_024454102.2 | chr4:g.105243571T>A | c.3596T>A | p.V1199E | RefSeq | GRCh38/hg38 |
XM_005263082.4 | chr4:g.105243571T>A | c.3596T>A | p.V1199E | RefSeq | GRCh38/hg38 |
Molecular Profile | Indication/Tumor Type | Response Type | Therapy Name | Approval Status | Evidence Type | Efficacy Evidence | References |
---|---|---|---|---|---|---|---|
TET2 mutant | acute myeloid leukemia | predicted - sensitive | Azacitidine | Phase I | Actionable | In a retrospective analysis, presence of a TET2 mutation correlated with higher overall response rate (ORR) in patients with myelodysplastic syndrome and acute myeloid leukemia following treatment with Vidaza (azacitidine), with an ORR of 85% (11/3) in TET2-mutated patients, compared to 47% (34/47) in patients with wild-type TET2, but did not correlate with overall survival (PMID: 21494260). | 21494260 |
TET2 mutant | myelofibrosis | not applicable | N/A | Guideline | Diagnostic | TET2 mutations aid in the diagnosis of primary myelofibrosis in the absence of JAK2, CALR, or MPL mutations (NCCN.org). | detail... |
TET2 mutant | acute myeloid leukemia | sensitive | Olaparib | Preclinical - Patient cell culture | Actionable | In a preclinical study, Lynparza (olaparib) treatment inhibited colony formation in patient-derived acute myeloid leukemia cells harboring a TET2 mutation along with FLT3-ITD and NPM1 mutation in culture (PMID: 34215619). | 34215619 |
TET2 mutant | angioimmunoblastic T-cell lymphoma | not applicable | N/A | Guideline | Diagnostic | TET2 mutations aid in the diagnosis of angioimmunoblastic T-cell lymphoma (NCCN.org). | detail... |
TET2 mutant | acute myeloid leukemia | not applicable | N/A | Clinical Study | Prognostic | In multiple clinical studies, including a meta-analysis, TET2 mutations were associated with shorter overall survival in patients with acute myeloid leukemia (PMID: 24524305, PMID: 25412851, PMID: 24994606). | 24524305 25412851 24994606 |